研究業績

研究業績2024年度 英文

詳細
Harada S, Azuma Y, Misumi Y, Hayashi H, Matsubara S, Nakahara K, Miyatake S, Matsumoto N, Ueda M. A Novel Mutation of VPS13D-related Disorders with Parkinsonism. Intern Med, 2024;63:2551-2553.

 

Kuyama N, Takashio S, Oguni T, Yamamoto M, Hirakawa K, Ishii M, Hanatani S, Matsuzawa Y, Usuku H, Yamamoto E, Ueda M, Tsujita K. Cardiac biomarker change at 1 year after tafamidis treatment predicts clinical outcomes in patients with transthyretin amyloid cardiomyopathy. J Am Heart Assoc, 2024;13:e034518.

 

Misumi Y, Yamashita T, Kuratomi A, Murakami Y, Fujita A, Matsumoto N, Ueda M. Long-term course of a case with a novel homozygous kyphoscoliosis peptidase variant. J Hum Genet, 2024;69:345-348.

 

Mizuguchi M, Nakagawa Y, Yokoyama T, Okada T, Fujii K, Takahashi K, Luan N, Nabeshima Y, Kanamitsu K, Nakagawa S, Yamakawa S, Ueda M, Ando Y, Toyooka N. Development of benziodarone analogues with enhanced potency for selective binding to transthyretin in human plasma. J Med Chem. 2024;67:6987-7005.

 

Nishizawa RH, Kawano H, Yoshimuta T, Eguchi C, Kojima S, Minami T, Sato D, Eguchi M, Okano S, Ikeda S, Ueda M, Maemura K. Effects of tafamidis on the left ventricular and left atrial strain in patients with wild-type transthyretin cardiac amyloidosis. Eur Heart J Cardiovasc Imaging. 2024;25:678-686.

 

Sasaki G, Uetani H, Nakaura T, Nakahara K, Morita K, Nagayama Y, Kidoh M, Iwashita K, Yoshida N, Hokamura M, Yamashita Y, Nakajima M, Ueda M, Hirai T. Optimizing High-Resolution MR Angiography: The Synergistic Effects of 3D Wheel Sampling and Deep Learning-Based Reconstruction. J Comput Assist Tomogr, 2024;48:819-825.

 

Suzuki Y, Tasaki M, Kakisaka K, Nishiya M, Nomura T, Nakao M, Sugawara E, Takikawa Y, Ueda M. Possible transmission of leukocyte chemotactic factor 2 amyloidosis after interpopulational liver transplantation. Amyloid, 2024;31:232-234.

 

Takahashi K, Iwamura T, Hiratsuka Y, Sasaki D, Yamamura N, Ueda M, Morioka H, Yoshino M, Enomoto D, Uemura S, Okura T, Sakaue T, Ikeda S. A Gluteus Medius Muscle Biopsy to Confirm Amyloid Transthyretin Deposition in Wild-type Transthyretin Cardiac Amyloidosis: A Report of Two Cases. Intern Med, 2024;63:1575-1584.

 

Urata M, Ito Y, Ogiya D, Kutsuzawa N, Ogura G, Ueda M, Hayama N, Oguma T, Asano K. Bilateral Hilar and Mediastinal Lymphadenopathy as an Initial Manifestation of Amyloidosis. Tokai J Exp Clin Med. 2024;49:12-16.

 

Usuku H, Yamamoto E, Sueta D, Shinriki R, Oike F, Tabata N, Ishii M, Hanatani S, Hoshiyama T, Kanazawa H, Arima Y, Takashio S, Kawano Y, Oda S, Kawano H, Ueda M, Tsujita K. A new staging system using right atrial strain in patients with immunoglobulin light-chain cardiac amyloidosis. ESC Heart Fail. 2024;11:1612-1624.

 

Yamasaki H, Kondo H, Shiroo T, Iwata N, Masuda T, Makita T, Iwabuchi Y, Tanazawa K, Takahashi M, Ono Y, Ogawa N, Harada T, Mitarai K, Yamauchi S, Takano M, Kodama N, Hirota K, Miyoshi M, Yonezu K, Tawara K, Abe I, Saito S, Fukui A, Fukuda T, Akioka H, Shinohara T, Akiyoshi K, Teshima Y, Yufu K, Daa T, Matsubara E, Asayama Y, Ueda M, Takahashi N. Efficacy of computed tomography-based evaluation of myocardial extracellular volume combined with red flags for early screening of concealed cardiac amyloidosis in patients with atrial fibrillation. Circ J, 2024;88:1167-1175.

 

Nomura T, Imamura M, Imura M, Mizutani H, Ueda M. Efgartigimod treatment for generalized myasthenia gravis: a single-center case series of 16 patients. Front Neurol, 2024;15:1472845.

 

Usuku H, Yamamoto E, Sueta D, Shinriki R, Oike F, Tabata N, Ishii M, Hanatani S, Hoshiyama T, Kanazawa H, Arima Y, Takashio S, Kawano Y, Oda S, Kawano H, Ueda M, Tsujita K. A new staging system using right atrial strain in patients with immunoglobulin light-chain cardiac amyloidosis. ESC Heart Fail, 2024;11:1612-1624.

 

Kuyama N, Takashio S, Oguni T, Yamamoto M, Hirakawa K, Ishii M, Hanatani S, Oda S, Matsuzawa Y, Usuku H, Yamamoto E, Hirai T, Ueda M, Tsujita K. Cardiac Biomarker Change at 1 Year After Tafamidis Treatment and Clinical Outcomes in Patients With Transthyretin Amyloid Cardiomyopathy. J Am Heart Assoc, 2024;13:e034518.

 

Yamasaki H, Kondo H, Shiroo T, Iwata N, Masuda T, Makita T, Iwabuchi Y, Tanazawa K, Takahashi M, Ono Y, Ogawa N, Harada T, Mitarai K, Yamauchi S, Takano M, Kodama N, Hirota K, Miyoshi M, Yonezu K, Tawara K, Abe I, Saito S, Fukui A, Fukuda T, Akioka H, Shinohara T, Akiyoshi K, Teshima Y, Yufu K, Daa T, Matsubara E, Asayama Y, Ueda M, Takahashi N. Efficacy of Computed Tomography-Based Evaluation of Myocardial Extracellular Volume Combined With Red Flags for Early Screening of Concealed Cardiac Amyloidosis in Patients With Atrial Fibrillation. Circ J, 2024;88:1167-1175.

 

Fukunari A, Matsushita H, Furukawa T, Matsuzaki H, Tanaka H, Ogawa Y, Sugimura Y, Inoue F, Ueda M, Ando Y. Arginine: A potential prophylactic supplement for transthyretin amyloidosis. Biochem Biophys Res Commun, 2024;737:150770.

 

Yagi S, Miyamoto R, Tasaki M, Morino H, Otani R, Kadota M, Ise T, Yamazaki H, Kusunose K, Yamaguchi K, Yamada H, Soeki T, Wakatsuki T, Fukuda D, Ueda M, Sata M. The APOA1 p.Leu202Arg variant potentially causes autosomal recessive cardiac amyloidosis. Hum Genome Var, 2024;11:30.

 

Takahashi K, Iwamura T, Sasaki D, Ueda M, Okura T. Wild-Type Transthyretin Amyloidosis With 99mTc-PYP Uptake in the Extracardiac Soft Tissues But Not in the Myocardium. Clin Nucl Med, 2024;49:1136-1138.

 

Mizutani H, Misumi Y, Ueda M. Teaching NeuroImage: Giant Tumefactive Perivascular Spaces: Longitudinal Follow-Up. Neurology. 2024;103:e209643.

 

Imura M, Nakahara K, Hara K, Yoshino H, Nishioka K, Hattori N, Ueda M. Rapidly Progressive Gait Disturbance and Extensive Iron Deposits in Late-Onset MPAN With a Pathogenic C19orf12 Variant: An 8-Year Follow-up. Neurology. 2024;103:e209724.

 

Honda K, Tasaki M, Yamano T, Ueda M, Naiki H, Tanaka N, Morinaga Y, Miyagawa-Hayashino A. High frequency of occult transthyretin and apolipoprotein AI-type amyloid in aortic valves removed by valve replacement for aortic stenosis. Amyloid. 2025;32:22-28.

 

Kuyama N, Izumiya Y, Takashio S, Tabira A, Hanatani S, Usuku H, Oda S, Matsuzawa Y, Yamamoto E, Ueda M, Tsujita K. Long-Term Outcomes of Tafamidis Treatment for Transthyretin Amyloid Cardiomyopathy in Two Patients. JACC Case Rep. 2024;29:102771.

 

Morikawa K, Izumiya Y, Takashio S, Kawano Y, Oguni T, Kuyama N, Oike F, Yamamoto M, Tabata N, Ishii M, Hanatani S, Hoshiyama T, Kanazawa H, Matsuzawa Y, Usuku H, Yamamoto E, Ueda M, Tsujita K. Early experience with daratumumab-containing regimens in patients with light-chain cardiac amyloidosis. J Cardiol. 2024 (in press).

 

Matsubara S, Nakajima M, Kaku Y, Mukasa A, Ueda M. Percutaneous Cerebral Angioplasty for Refractory Middle Cerebral Artery Stenosis Due to Varicella-Zoster Virus-Related Vasculopathy: A Case Report. Cureus. 2024;16:e69773.

 

Murakami H, Mizutani H, Nakahara K, Uetani H, Kaku Y, Nakajima M, Mukasa A, Hirai T, Ueda M. Utilization of Heavily T2-Weighted Imaging and Dynamic Contrast-Enhanced 3T Magnetic Resonance Angiography for Diagnosing Spinal Extradural Arteriovenous Fistula: A Case Report. Cureus. 2024;16:e76708.

 

Oguni T, Takashio S, Kuyama N, Hirakawa K, Hanatani S, Oike F, Usuku H, Matsuzawa Y, Kidoh M, Oda S, Yamamoto E, Ueda M, Hirai T, Tsujita K. Clinical characteristics of patients with high extracellular volume fraction evaluated by cardiac computed tomography for coronary artery evaluation. Eur Heart J Open. 2024;4:oeae036.

 

Mizutani H, Nakahara K, Ueda M. Early Diagnosis of WEBINO (Wall-Eyed Bilateral Internuclear Ophthalmoplegia) Syndrome Using Thin-Slice Gapless Diffusion-Weighted Imaging in an Acute Ischemic Stroke Patient: A Case Report. Cureus. 2024;16:e73372.

 

Shindo S, Uchida K, Yoshimura S, Sakai N, Yamagami H, Toyoda K, Matsumaru Y, Matsumoto Y, Kimura K, Ishikura R, Inoue M, Sakakibara F, Nakajima M, Ueda M, Morimoto T. Intravenous alteplase before endovascular therapy for acute large vessel occlusion with large ischemic core: subanalysis of a randomized clinical trial. J Neurointerv Surg. 2024;16:1094-1100.

 

Namitome S, Nagao Y, Shigehatake Y, Matsuo J, Kawamoto K, Kuroki K, Hayashi H, Nakajima M, Terasaki T, Ueda M, Shindo S. Evaluation of partial resheathing of EmboTrap III using the microcatheter (PREMIER) technique for fibrin-rich hard clots in an in vitro vessel model. Front Neurol. 2024;15:1368890.

 

Mizutani H, Nakajima M, Ueda M. Delayed cerebral complications associated with endovascular catheter coil embolization for pulmonary venous shunts mimicking cerebral inflammatory diseases. Heliyon. 2024;10:e33541.

 

Adams D, Wixner J, Polydefkis M, Berk JL, Conceição IM, Dispenzieri A, Peltier A, Ueda M, Bender S, Capocelli K, Jay PY, Yureneva E, Obici L; patisiran Global OLE study group. Five-Year Results With Patisiran for Hereditary Transthyretin Amyloidosis With Polyneuropathy: A Randomized Clinical Trial With Open-Label Extension. JAMA Neurol, 2025;82:228-236.

 

Sugata K, Takatori M, Reda O, Tan BJY, Tokunaga M, Sato T, Ueda M, Yamano Y, Utsunomiya A, Satou Y. Effect of Viral Antigen Mismatch on Antiviral T-Cell Response and Immunotherapeutic Efficacy Against Adult T-Cell Leukemia/Lymphoma. J Infect Dis. 2025;231:816-821.

 

Usuku H, Yamamoto E, Miyazaki K, Higashi R, Nozuhara A, Oike F, Kuyama N, Tabata N, Ishii M, Hanatani S, Hoshiyama T, Kanazawa H, Sueta D, Arima Y, Oda S, Kawano H, Matsuzawa Y, Izumiya Y, Ueda M, Tanaka Y, Tsujita K. Clinical significance of the estimation of pulmonary-right ventricular uncoupling in patients with transthyretin amyloid cardiomyopathy. Eur Heart J Imaging Methods Pract. 2025;qyae113.

 

Kuyama N, Izumiya Y, Takashio S, Usuku H, Tabira A, Oguni T, Yamamoto M, Hirakawa K, Ishii M, Tabata N, Hoshiyama T, Kanazawa H, Hanatani S, Kidoh M, Oda S, Matsuzawa Y, Yamamoto E, Hirai T, Ueda M, Tsujita K. Long-Term Effect of Tafamidis on Clinical Parameters and Prognostic Predictors in Patients With Transthyretin Amyloid Cardiomyopathy. Circ J. 2025;89:421-431.

 

Mizutani H, Misumi Y, Hamanaka K, Tawara N, Miyatake S, Matsumoto N, Ueda M. A Case of Nebulin-Related Nemaline Myopathy With Asymmetric Distal Lower Limb Weakness. Cureus. 2025;17:e78945.

 

Honda Y, Nomura T, Nakahara K, Matsuo J, Shirahama R, Kuroki K, Ueda M. A Case of Multiple Intracranial Hemorrhages Due to Biopsy-Proven Varicella Zoster Virus Vasculopathy Without Rash. Cureus. 2025;17:e77890.

 

Copyright© Department of Neurology, Graduate School of Medical Sciences, Kumamoto University.